Schinzel-Giedion syndrome: a case with sacrococcygeal teratoma and cor-triatriatum dexter
نویسندگان
چکیده
Schinzel-Giedion syndrome which is associated with midfacial hypoplasia and coarse dysmorphic features is a multiple congenital malformation syndrome. It is believed that risk of malignancy may be a component of the anomaly. We report herein a case of a 16 months old boy with SGS associated with sacrococcygeal teratoma and cor-triatriatum dexter. Histopathology report of the excised sacrococcygeal mass showed no malignant foci. He was however lost to follow up in the second week post-operation. Pan African Medical Journal. 2017; 26:30 doi:10.11604/pamj.2017.26.30.11525 This article is available online at: http://www.panafrican-med-journal.com/content/article/26/30/full/ © Lofty-John Anyanwu et al. The Pan African Medical Journal ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Pan African Medical Journal – ISSN: 19378688 (www.panafrican-med-journal.com) Published in partnership with the African Field Epidemiology Network (AFENET). (www.afenet.net) Case report Open Access
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